1914b79420bc828e04a1b997a46f61b04798eb91
History.md
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| 1 | + |
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| 2 | +## History |
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| 3 | + |
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| 4 | +```mermaid |
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| 5 | +%%{init: { 'logLevel': 'debug', 'theme': 'dark' } }%% |
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| 6 | +timeline |
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| 7 | + title Publication timing |
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| 8 | + 1992-01-01 : Tanaka : DLBCL |
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| 9 | + 2011-07-27 : Morin : FL |
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| 10 | + 2021-04-01 : Sarkozy : PMBL |
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| 11 | + 2022-07-06 : Burkhardt : BL |
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| 12 | +``` |
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| ... | ... | \ No newline at end of file |
Overview.md
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| 1 | +## Overview |
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| 2 | + |
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| 3 | +BCL2 mutations are frequently found in DLBCL, particularly in the germinal center B-cell (GCB) subtype, and are often located in the flexible loop domain and outside the BCL2-homology domains. |
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| 4 | +These mutations are caused by the somatic hypermutation process. The presence of these mutations are strongly correlated with the presence of a translocation between BCL2 and one of the immunoglobulin loci. |
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| 5 | +Although missense mutations may not be under positive selective pressure in the context of lymphomagenesis, some of these mutations may interfere with the function of BCL2 antagonists. |
Template.md
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| 1 | +--- |
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| 2 | +bibliography: 'morinlab.bib' |
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| 3 | +csl: 'NLM.csl' |
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| 4 | +link-citations: true |
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| 5 | +--- |
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| 6 | +# BCL2 |
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| 7 | + |
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| 8 | +[[include:Overview.md]] |
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| 9 | + |
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| 10 | +[[include:History.md]] |
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| 11 | + |
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| 12 | +## Relevance tier by entity |
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| 13 | + |
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| 14 | +|Entity|Tier|Description | |
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| 15 | +|:------:|:----:|--------------------------------------| |
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| 16 | +| |1[@balSuperenhancerHypermutationAlters2022] |high-confidence DLBCL gene [@tanakaFrequentIncidenceSomatic1992]| |
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| 17 | +| |1 |high-confidence FL gene| |
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| 18 | +||2|relevance in PMBL/cHL/GZL not firmly established[@sarkozyMutationalLandscapeGray2021]| |
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| 19 | +| |2 |relevance in BL not firmly established[@burkhardtClinicalRelevanceMolecular2022]| |
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| 20 | + | |
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| 21 | + |
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| 22 | +## Mutation incidence in large patient cohorts (GAMBL reanalysis) |
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| 23 | + |
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| 24 | +[[include:DLBCL_BCL2.md]] |
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| 25 | +[[include:FL_BCL2.md]] |
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| 26 | +[[include:BL_BCL2.md]] |
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| 27 | + |
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| 28 | + |
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| 29 | +## Mutation pattern and selective pressure estimates |
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| 30 | + |
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| 31 | +|Entity|aSHM|Significant selection|dN/dS (missense)|dN/dS (nonsense)| |
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| 32 | +|:------:|:----:|:---------------------:|:----------------:|:----------------:| |
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| 33 | +|BL |Yes |No |0.000 |0 | |
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| 34 | +|DLBCL |Yes |Yes |2.645 |0 | |
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| 35 | +|FL |Yes |No |1.197 |0 | |
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| 36 | + |
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| 37 | +## aSHM regions |
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| 38 | + |
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| 39 | +|chr_name|hg19_start|hg19_end|region |regulatory_comment| |
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| 40 | +|:--------:|:----------:|:--------:|:---------------------------------------------------------------------------------------------:|:------------------:| |
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| 41 | +|chr18 |60796984 |60814103|[intron](https://genome.ucsc.edu/s/rdmorin/GAMBL%20hg19?position=chr18%3A60796984%2D60814103)|strong_enhancer | |
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| 42 | +|chr18 |60982728 |60988342|[TSS](https://genome.ucsc.edu/s/rdmorin/GAMBL%20hg19?position=chr18%3A60982728%2D60988342) |active_promoter | |
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| 43 | + |
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| 44 | + |
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| 45 | + |
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| 46 | +## BCL2 Hotspots |
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| 47 | + |
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| 48 | +| Chromosome |Coordinate (hg19) | ref>alt | HGVSp | |
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| 49 | + | :---:| :---: | :--: | :---: | |
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| 50 | +| chr18 | 60985854 | T>C | M16V | |
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| 51 | +| chr18 | 60985854 | T>A | M16L | |
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| 52 | +| chr18 | 60985853 | A>T | M16K | |
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| 53 | +| chr18 | 60985852 | C>T | M16I | |
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| 54 | +| chr18 | 60985849 | C>G | K17N | |
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| 55 | +| chr18 | 60985842 | G>A | H20Y | |
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| 56 | +| chr18 | 60985840 | A>C | H20Q | |
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| 57 | +| chr18 | 60985838 | T>G | Y21S | |
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| 58 | +| chr18 | 60985835 | T>C | K22R | |
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| 59 | +| chr18 | 60985834 | CT>TC | K22R | |
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| 60 | + |
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| 61 | +View coding variants in ProteinPaint [hg19](https://morinlab.github.io/LLMPP/GAMBL/BCL2_protein.html) or [hg38](https://morinlab.github.io/LLMPP/GAMBL/BCL2_protein_hg38.html) |
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| 62 | + |
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| 63 | + |
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| 64 | + |
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| 65 | +View all variants in GenomePaint [hg19](https://morinlab.github.io/LLMPP/GAMBL/BCL2.html) or [hg38](https://morinlab.github.io/LLMPP/GAMBL/BCL2_hg38.html) |
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| 66 | + |
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| 67 | + |
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| 68 | + |
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| 69 | + |
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| 70 | +## BCL2 Expression |
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| 71 | + |
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| 72 | + |
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| 73 | +<!-- ORIGIN: 1339299 --> |
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| 74 | +<!-- FL: morinFrequentMutationHistonemodifying2011 --> |
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| 75 | +<!-- BL: burkhardtClinicalRelevanceMolecular2022b --> |
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| 76 | +<!-- BL: burkhardtClinicalRelevanceMolecular2022b --> |
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| 77 | +<!-- DLBCL: tanakaFrequentIncidenceSomatic1992 --> |