ac256a7b0fc09340c562e0f55b9f315beb01d5ef
BCL7A.md
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| 2 | 2 | |
| 3 | 3 | ## Overview |
| 4 | 4 | |
| 5 | -BCL7A protein interacts with components of the SWI/SNF chromatin remodeling complex, implicating it in chromatin remodeling processes essential for normal cellular function.<sup>1</sup> Mutations in the BCL7A gene have been identified in diffuse large B-cell lymphoma (DLBCL) and other B-cell lymphomas, implicating this gene in the pathogenesis of these cancers. Importantly, BCL7A is one of [a number of genes](https://github.com/morinlab/LLMPP/wiki/ashm) affected by aberrant somatic hypermutation in B-cell lymphomas, which complicates the interpretation of mutations at this locus. Due to the presence of some loss-of-function mutations, BCL7A has been described as a tumour-suppressor gene in DLBCL.<sup>2</sup> The rate of DLBCLs with biallelic loss of this locus remains unclear. |
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| 6 | - |
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| 7 | -## History |
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| 8 | -Mutations in this gene were first described in FL in 2017 by Krysiak et al.<sup>3</sup> Mutations were described in DLBCL in 2018 by Arthur et al<sup>4</sup> and in BL in 2019 by Grande et al.<sup>5</sup> |
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| 5 | +BCL7A protein interacts with components of the SWI/SNF chromatin remodeling complex, implicating it in chromatin remodeling processes essential for normal cellular function.<sup>1</sup> Mutations in the BCL7A gene have been identified in diffuse large B-cell lymphoma (DLBCL) and other B-cell lymphomas, implicating this gene in the pathogenesis of these cancers. Importantly, BCL7A is one of [a number of genes](https://github.com/morinlab/LLMPP/wiki/ashm) affected by aberrant somatic hypermutation in B-cell lymphomas, which complicates the interpretation of mutations at this locus. Due to the presence of some loss-of-function mutations, BCL7A has been described as a tumour-suppressor gene in DLBCL. The rate of DLBCLs with biallelic loss of this locus remains unclear. |
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| 11 | 8 | ```mermaid |
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| 23 | 20 | |Entity|Tier|Description | |
| 24 | 21 | |:------:|:----:|--------------------------------------| |
| 25 | 22 | ||1|high-confidence MZL gene| |
| 26 | -||2|relevance in PMBL/cHL/GZL not firmly established| |
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| 27 | -| |1-a | aSHM target and high-confidence DLBCL gene | |
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| 28 | -| |1-a | aSHM target and high-confidence FL gene | |
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| 29 | -| |2-a | aSHM target; Although recurrent, the relevance of mutations in BL is tenuous | |
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| 23 | +||2|relevance in PMBL/cHL/GZL not firmly established[@reichelFlowSortingExome2015a]| |
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| 24 | +| |1-a | aSHM target and high-confidence DLBCL gene [@arthurGenomewideDiscoverySomatic2018] | |
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| 25 | +| |1-a | aSHM target and high-confidence FL gene [@krysiakRecurrentSomaticMutations2017b] | |
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| 26 | +| |2-a | aSHM target; Although recurrent, the relevance of mutations in BL is tenuous [@grandeGenomewideDiscoverySomatic2019]| |
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| 30 | 27 | |
| 31 | 28 | |
| 32 | 29 | ## Mutation incidence in large patient cohorts (GAMBL reanalysis) |