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FBXO11.md
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| 1 | 1 | # FBXO11 |
| 2 | 2 | ## Overview |
| 3 | -Somatic mutations in FBXO11 are common in BL<sup>1,2</sup> and appear in a small number of DLBCLs.<sup>3</sup> Mutations lead to stabilization of BCL6, an important transcriptional repressor involved in lymphomagenesis.<sup>4</sup> These mutations present a potential novel target for therapeutic intervention, particularly through strategies aimed at degrading BCL6 or inhibiting its function.<sup>4</sup> |
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| 3 | +Somatic mutations in FBXO11 are common in BL<sup>1,2</sup> and appear in a small number of DLBCLs.<sup>3</sup> This gene has some recurrent sites of mutations (hot spots). Mutations lead to stabilization of BCL6, an important transcriptional repressor involved in lymphomagenesis.<sup>4</sup> These mutations present a potential novel target for therapeutic intervention, particularly through strategies aimed at degrading BCL6 or inhibiting its function.<sup>4</sup> |
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| 4 | 4 | |
| 5 | 5 | ## Relevance tier by entity |
| 6 | 6 | |
| ... | ... | @@ -33,6 +33,25 @@ Somatic mutations in FBXO11 are common in BL<sup>1,2</sup> and appear in a small |
| 33 | 33 | > [!NOTE] |
| 34 | 34 | > First described in BL in 2015 by Pighi et al<sup>1</sup> and described in DLBCL in 2021 by Hübschmann et al.<sup>5</sup> |
| 35 | 35 | |
| 36 | +## FBXO11 hot spots |
|
| 37 | +|Chromosome|Coordinate|Mutation|HGVSp| |
|
| 38 | +|:-:|:-:|:-:|:-:| |
|
| 39 | +|chr2|48040426|T>A|N725I| |
|
| 40 | +|chr2|48040427|T>C|N725D| |
|
| 41 | +|chr2|48040427|T>G|N725H| |
|
| 42 | +|chr2|48040427|T>A|N725Y| |
|
| 43 | +|chr2|48040488|TA>GC|I704S| |
|
| 44 | +|chr2|48040489|A>C|I704R| |
|
| 45 | +|chr2|48040495|T>A|N702I| |
|
| 46 | +|chr2|48040495|T>C|N702S| |
|
| 47 | +|chr2|48040496|T>C|N702D| |
|
| 48 | +|chr2|48040496|T>A|N702Y| |
|
| 49 | +|chr2|48040500|T>A|E700D| |
|
| 50 | +|chr2|48040500|T>G|E700D| |
|
| 51 | +|chr2|48040501|T>A|E700V| |
|
| 52 | +|chr2|48040510|C>T|G697D| |
|
| 53 | +|chr2|48040511|C>G|G697R| |
|
| 54 | + |
|
| 36 | 55 | |
| 37 | 56 | View coding variants in ProteinPaint [hg19](https://morinlab.github.io/LLMPP/GAMBL/FBXO11_protein.html) or [hg38](https://morinlab.github.io/LLMPP/GAMBL/FBXO11_protein_hg38.html) |
| 38 | 57 |